N-carbamyl-β-aminoisobutyrateNCβAIBAN-carbamyl-β-alanineβ-ureidopropionase (βUP) deficiency
…egradation metabolites, such as N-carbamyl-β-alanine (NCβA) and N-carbamyl-β-aminoisobutyrate (NCβAIBA), which are not widely available in routine clinical p…