Alagille syndromealpha1-antitrypsin deficiencylow phospholipid-associated cholelithiasisintrahepatic cholestasis of pregnancybenign recurrent intrahepatic cholestasisPFICIBATiursodeoxycholic acidintestinal bile acid transporter inhibitors
…cause PFIC types 1–3. Several other congenital diseases such as Alagille syndrome and alpha1-antitrypsin deficiency comprise cholestatic pruritus…