96.3%
VEXAS syndromerheumatoid arthritiscorticosteroids
…VEXAS syndrome (vacuoles, E1 enzyme, X-linked, autoinflammatory and somatic) i…
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This disease is selected. Its supporting articles are shown below.
…VEXAS syndrome (vacuoles, E1 enzyme, X-linked, autoinflammatory and somatic) i…
…enetic testing confirmed a UBA1 p.Met41Thr mutation, confirming VEXAS syndrome. We gave intravenous methylprednisolone, then oral prednisolone…