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This report focuses on a female infant without relevant prenatal or familial medical history. The general practitioner noticed a bilateral exophthalmia and nasal obstruction without respiratory distress on a regular child surveillance consultation and referred her to a paediatric consultation. On physical examination, she presented with bilateral ocular proptosis, hypertelorism and a broad nasal bridge. She was referred to ophthalmology, and an ophthalmic examination of the right eye fundus showed an enlarged, funnel-shaped cavity of the optic disc and a radial arrangement of retinal blood vessels. Those findings were compatible with Morning-Glory syndrome ( figure 1). An MRI of the brain was carried out, and a sphenoethmoidal meningocele 16 mm in size, without an encephalocele, was revealed (figure 2). Systemic examination was unremarkable and ruled out dysfunction of the hypothalamic-pituitary axis. A genetic evaluation was performed, including array-CGH testing, which revealed no pathogenic copy number variations. The patient was referred to neurosurgery. No history of CSF fistula was apparent and the parents were advised on recommendations and alarm signs and repair surgery after 1 year of age to minimise complications from anaesthesia.